Pulmonary manifestations of systemic vasculitis in childhood

Otolaryngologic manifestations of systemic vasculitis.

Systemic vasculitis is a heterogeneous group of diseases of various aetiologies and manifestations. In general, the clinical results derive from ischemia caused by vascular inflammation, which depends on the organ affected. Such vasculitis cases are classified according to the classification of the Chapel Hill conference. They can present with relative frequency as ENT manifestations in both th...

Audiovestibular Manifestations in Systemic Vasculitis: An Update

The kaleidoscopic manifestations of systemic vasculitis.

The IXth Menarini International Symposium on Autoimmunity took place in Seville (Spain) in December 2010, and focused on “The kaleidoscopic manifestations of systemic vasculitis”, addressing both pathogenic and clinical aspects of Anti-Neutrophil Cytoplasmic Autoantibody-Associated Systemic Vasculitis (AASV). Moreover, two specific topics related to primary angiitis of the central nervous syste...

Idiopathic pulmonary fibrosis and p-ANCA positivity predating manifestations of systemic vasculitis

The occurrence of perinuclear anti-neutrophilic cytoplasmic antibodies (p-ANCA) in pulmonary fibrosis has been reported in a number of small studies, however, the appearance of p-ANCA in already established idiopathic pulmonary fibrosis (IPF), predating the manifestations of vasculitis has not been widely appreciated. We report 2 cases with radiographic evidence of established IPF where p-ANCA ...

Imaging techniques for the evaluation of systemic manifestations of vasculitis

Vasculitis create a local inflammatory process in the vessel wall, which determines the different organic manifestations according to vessel size and location. Imaging techniques play a key role in the characterization and detection of large and medium size vessel vasculitis. Imaging is able to detect the vessel wall edema and to monitor the therapeutic response. In small vessel vasculitis, ima...